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Table 1 Ocular findings in Parry Romberg disease

From: Parry Romberg syndrome with a wide range of ocular manifestations: a case report

Ocular structure

Ocular manifestation

Orbit

Enophtalmos [730]

Orbital neurinoma [31]

Extraocular muscles

Third nerve paralysis (ipsi or controlateral) [13]

Muscle thinning [32]

Exo-eso-ipotropia [3335]

Diplopia [33]

Restrictive strabismus [36]

Eyelids

Retraction [35]/lagophthalmos

Atrophy [23], Pseudoptosis [37]

Cornea

Band keratopathy [30, 38]

Exposure keratopathy [39]

Primary endothelial failure [40]

Ipoestesia [30]

Endothelial precipitates [41]

Flourlike stromal deposits [42]

Iris/Uvea

Uveitis [20]

Fuchs heterochromic iridocyclitis [38]

Iris atrophy (our case, [33, 43])

Lens

Cataract [38]

Lens dislocation (our case, [26])

Ciliary body

Hypotony/phtisis [27]

Atrophy (our case, [26])

Glaucoma [28]

Vitreous

Bilateral vireitis [44]

Retina

Retinal vasculitis [45, 46]

Retinal telangiectasia [32]

Retinal pigment epithelial changes [34]

Retinal detachment [47]

Coats disease [44, 47]

Chorioretinal lesions [48]

Central retinal artery occlusion [49]

Optic nerve

Papillitis [44]/neuroretinitis [44]

Neuro-ophthalmic

Horner syndrome [21]

Adie pupil [25]

Mydriase/miosis [21]