Zimmerman, 1988 [6]
|
13/M
|
OS
|
Superior epibulbar nodule (8 × 6 mm)
|
Minimal inguinal lymphadenopathy
|
Excision
|
No
|
Tan, 2002 [7]
|
63/M
|
OS
|
Inferior epibulbar nodule (5 × 12 mm), anterior modular scleritis, anterior and posterior uveitis
|
Post-auricular lymphadenopathy and vocal cord nodule
|
Excision + Oral & topical steroid
|
Yes
|
Albini, 2005 [8]
|
71/M
|
OD
|
Nasal side epibulbar nodule (15 × 15 mm)
|
Nil
|
Excision
|
No
|
|
51/M
|
OS
|
Nasal side epibulbar nodule (5 mm)
|
Nil
|
Excision
|
No
|
Sarwal, 2008 [9]
|
53/F
|
OU
|
Superotemporal epibulbar nodule (3 × 3 mm), anterior nodular scleritis, anterior uveitis
|
Anterior chest wall, abdominal and pelvic masses
|
Excision + topical steroid
|
Yes
|
|
19/F
|
OS
|
Superonasal epibulbar nodule (3.25 × 3.25 mm), nodular scleritis
|
Nil
|
Excision
|
No
|
Fernandes, 2008 [10]
|
19/M
|
OD
|
Temporal epibulbar nodule (12 × 11 mm), conjunctival injection
|
Nil
|
Excision
|
Yes
|
Maheshwari, 2008 [11]
|
17/M
|
OS
|
Temporal epibulbar nodule (3 × 5 mm)
|
Nil
|
Excision + oral steroid
|
No
|
De Oliveira, 2011 [3]
|
14/F
|
OD
|
Inferior epibulbar nodule (5 × 15 mm), conjunctival injection
|
Nil
|
Excision
|
No
|
Payne, 2011 [4]
|
20/F
|
OS
|
Inferonasal epibulbar nodule (5 × 5 mm), panuveitis, subretinal exudate
|
Pelvic mass
|
Excision + Oral & topical steroid
|
Yes
|
Shah, 2012 [12]
|
36/F
|
OS
|
Superior epibulbar nodule (12 × 20 mm), trace anterior uveitis
|
Nil
|
Excision + Oral & topical steroid + oral cyclosporine
|
Yes
|
Choi, 2018 [2]
|
35/M
|
OU
|
Epibulbar masses, retinal detachment, and choroidal effusions
|
Sinus, trachea, renal, subcutaneous skin lesions
|
Cladribine, steroids, mycophenolate mofetil, rituximab, vemurafenib
|
Yes
|
|
54/F
|
OU
|
Epibulbar masses
|
Colon lesions, peritoneum, soft tissue of chest wall
|
Excision
|
Unknown
|
|
41/F
|
OU
|
Epibulbar masses
|
Lung, aortic lymph nodes, pleura, skeletal (rib)
|
Steroid
|
Unknown
|
Lee, 2018 (Present case)
|
36/M
|
OS
|
Antecedent uveitis and anterior nodular scleritis, inferotemporal epibulbar mass
|
Facial skin nodule, multiple papulonodules on bilateral cheek, ear and scalp
|
Excision + Oral & topical steroid, methotrexate
|
No
|