Fig. 6

Full field electroretinography showed a diminished 0.1 rod isolated ERG b-wave bilaterally, consistent with severely decreased rod function; b scotopic 3.0 ERG with depressed combined rod-cone response in the right eye and 10% of normal a- and b-waves in the left eye; c residual 3.0 ERG cone response with 5% normal amplitude and delayed peak implicit time bilaterally; d photopic 3.0 32 Hz flicker reduced to 10% normal amplitude and delayed implicit time bilaterally