Fig. 1

Serial external eye photography of Patient 1 before and after diagnosis of granulomatosis with polyangiitis (GPA). a. Initial presentation of superior nasal conjunctiva congestion (OD) with a 5-mm superior conjunctival ulceration and a 9 to 12 o’clock peripheral ulcerative keratitis was noted with visual acuity (VA) was 0.09. The insert shows fluorescein staining of some tiny epithelial defects and diffuse superficial punctate staining of the cornea. b. Initial presentation of superior conjunctival congestion and limbo-corneal neovascularization (OS) was noted with VA of 0.1. The insert shows fluorescein staining of mild superficial punctate staining of the cornea. c.d. Six months after initial presentation (i.e. 4 months after right eye cataract surgery), resolution in conjunctiva congestion (OU), peripheral ulcerative keratopathy (OD) and limbo-corneal neovascularization (OS) was noted with VA of 0.6 (OD) and 0.2 (OS) respectively