Fig. 4

This middle-aged patient had BCVA of 20/50 (OD) and 20/1000 (OS). a Color fundus revealed a greenish background color with depigmentation. b Obvious sclerotic vessels were evident on NIR (yellow arrows). Multiple hyperreflective crystal deposits could still be observed. c On OCT, a small foveal preservation island was demonstrated in the right eye. OCT of the left eye showed destruction of EZ and ONL. A normal/hyper-AF area on AF cannot predict structural preservation on OCT. The white star indicates the area of outer nuclear layer thinning and EZ disruption seen on OCT, but it corresponded to neither hypo-AF nor normal AF. d The foveal structures are labeled in high magnification from red squares in (c) (NFL nerve fiber layer; GCL ganglion cell layer; IPL inner plexiform layer; INL inner nulear layer; OPL outer plexiform layer; ONL outer nuclear layer; ELM external limiting membrane; EZ ellipsoid zone; RPE retinal pigment epithelium)