Fig. 5

It is hard to recognize a central island on FAF because of the hypo-AF at the fovea. a, b The patients with preserved foveal structures, especially EZ, on OCT had a BCVA of 20/20. c OCT shows central destruction of the EZ. This eye had a BCVA of 20/100. On FAF, it was relatively difficult to determine whether the central area was preserved. d The preserved island of the normal retinal structure was eccentric. On OCT, a red arrow indicates the central fovea, but the EZ starts from the site where the yellowish arrow indicates the nasal retina. FAF shows confluent patches. The BCVA of this eye was 20/67 (FAF fundus autofluorescence; OCT optical choherence tomography; BCVA best corrected visual acuity; EZ ellipsoid zone)