Table 1 Ocular findings in patients with FMNS with infantile unilateral visual loss
From: Effects of extraocular muscle surgery in children with monocular blindness and bilateral nystagmus
Patient/Sex/Age at surgery (years) | Cause of monocularity | Pre-operative situation | Surgical Procedure (millimeters) | Post-operative situation | Follow up(months) | ||||||
|---|---|---|---|---|---|---|---|---|---|---|---|
BCVA (with optimum head posture) | Characteristics of Nystagmus | Abnormal head posture (Degrees) | Eye alignment (D/N, prism diopters) | BCVA (with optimum head posture) | Characteristics of Nystagmus | Abnormal head posture (Degrees) | Eye alignment (D/N, prism diopters) | ||||
1/M/10 | L: congenital corneal opacity | R: 20/20 | jerk nystagmus, null zone in left gaze | 18° right face turn | 0/-8 | R: MR recess 5/LR resect 8 | R: 20/20 | jerk nystagmus, null zone in PP | none | 0/0 | 3 |
L: 20/4000 | L: MR resect 6/LR recess 7 | L: 20/4000 | |||||||||
2/M/8 | L: corneal dermoid | R: 20/25 | jerk nystagmus, null zone in left gaze | 15° right face turn, 10° right head tilt | 0/0 | R: MR recess 7/LR resect 10 | R: 20/25 | jerk nystagmus, null zone in slight left gaze | 5° right face turn, 8° right head tilt | 0/0 | 12 |
L: NLP | L: NLP | ||||||||||
3/M/6 | L: congenital | R: 20/30 | jerk nystagmus, null zone in left gaze | 35° right face turn,15° right head tilt | -10/-10 | R: MR recess 6/LR resect 8 | R: 20/25 | jerk nystagmus, | none | 0/0 | 23 |
microphthalmus | L: LP | L: MR resect 6/LR recess 8 | L: LP | null zone in PP | |||||||
4/F/21 | R: optic nerve hypoplasia | R: 20/200 | jerk nystagmus, null zone in right gaze | 20° left face turn | +35/+35 | R/L: MR recess 4.5 | R: 20/200 | jerk nystagmus, null zone in PP | none – 10° left face turn | 0/0 | |
L: 20/20 | L: 20/20 | ||||||||||
R: optic nerve hypoplasia | jerk nystagmus, null zone in right gaze | 25° left face turn | +4/+4 | R: LR recess 5.5 L: MR recess 5.5 | jerk nystagmus, null zone in slight right gaze | 12° left face turn | -5/-5 | 202 | |||
5/F/52 | R: optic nerve hypoplasia | R: LP | jerk nystagmus, null zone in right gaze | 35° left face turn, 15° left head tilt | +55/+55 | L: MR recess 6/LR resect 8 | R: LP | jerk nystagmus, null zone in PP | 15° left head tilt | +20/+25 | |
L: 20/20 | L: 20/20 | ||||||||||
R: optic nerve hypoplasia | R: LP | jerk nystagmus, null zone in right gaze | 20° left face turn, 15° left head tilt | +35/+35 | R: MR recess 6/LR resect 6 | R: LP | jerk nystagmus, null zone in PP | 10° left head tilt | 0/+6 | 60 | |
L: 20/25 | L: 20/20 | ||||||||||
6/F/18 | L: congenital cataract and microphthalmus | R: 20/20 | jerk nystagmus, null zone in left gaze | 12° right face turn | +45/+45 | R: MR recess 5/LR resect 7 | R: 20/20 | jerk nystagmus, null zone in PP | none | 0/0 | 3 |
L: LP | L: LP | ||||||||||
7/M/16 | R: congenital microphthalmus | R: NLP | jerk nystagmus, null zone in right and up-gaze | 10° left face turn 20° right head tilt 15° chin down posture | +45/+45 | L: SO tuck 9 mm | R: NLP | null zone in PP | 5° right head tilt | 0/0 | 12 |
L: 20/20 | L/R 25 | IO anteroposition | L: 20/20 | ||||||||
LR resect 8 and full tendon width downward shift | |||||||||||
8/F/9 | R: congenital microphthalmus | R: LP | jerk nystagmus, null zone in right gaze | 30° left face turn, 3° chin down posture | +55/+55 | L: MR recess 6.5 / LR resect 10 | R: LP | jerk nystagmus, null zone in PP | 5° left face turn | +8/+8 | 3 |
L: 20/25 | L: 20/25 | ||||||||||
9/M/4 | L: retinal hamartoma | R: 20/25 | jerk nystagmus, null zone in left gaze | 35° right face turn | +55/+55 | R: MR recess 6/LR resect 8 | R: 20/25 | jerk nystagmus, null zone in left gaze | 20° right face turn | +8/+20 | 12 |
L: 20/400 | L: 20/400 | ||||||||||