Table 1 PEDBD criteria and ICBD criteria

PEDBD criteria

Score ≥ 3 indicates pediatric Behçet’s disease

Item

Description

Points

Recurrent oral aphthosis

At least three attacks/year

1

Genital ulceration

Typically with scar

1

Skin involvement

Necrotic folliculitis, acneiform lesions,erythema nodosum

1

Ocular involvement

Anterior uveitis, posterior uveitis, retinal vasculitis

1

Neurological signs

With the exception of isolated headaches

1

Vascular signs

Venous thrombosis, arterial thrombosis,arterial aneurysm

1

ICBD criteria

Score ≥ 4 indicates Behçet’s diagnosis

Item

Description

Points

Oral aphtosis

Not specified

2

Genital aphtosis

Not specified

2

Ocular lesions

Anterior uveitis, posterior uvitis or retinal vasculitis

2

Skin lesions

Pseudofolliculitis, skin aphtosis, erythema nodosum

1

Neurological manifestations

Not specified

1

Vascular manifestations

Arterial thrombosis, large vein thrombosis, phlebitis or superficial phlebitis

1

Positive pathergy test

Not specified

1