Table 2 Patients characteristics at the onset of uveitis. M = male, F = female, MP = methyliprendisolone
Case # | Age/ gender | Descent | BCVA at presentation (logMar) | Final BCVA (logMAR) | Presenting symptoms | Diagnostic delay (months) | Systemic features | Associated conditions | Anterior / Posterior uveitis | Retinal vasculitis | Ocular Complications | Systemic Treatments | Ophthalmic Treatments | PEDBD criteria fulfilled | ICBD criteria fulfilled | Follow-up (months) |
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
1 | 13 / M | Northern Africa HLAB51 + | OD: 0 OS: 2.3 | OD: 0 OS: 0 | Ocular | 18 | Oral aphtosis pseudofolliulitis | Hétérozygous M694I | - / + | + | Macular edema Serous retinal detachment Necrotizing retinitis Occlusive vasculitis | Intravenous MP pulse 15 mg/kg and oral prednisone Infliximab 5 mg/kg Azathioprine 2 mg/kg/day Colchicine 1 mg/day | Hourly dexamethasone eye drops Tropicamide and phenylephrine eye drops | + | + | 69 |
2 | 9 / M | Northern Africa HLAB51 + | OD: 0.4 OS: 1.9 | OD: 0 OS: 0.1 | Ocular | 0.3 | Oral aphtosis Meningitidis Anorexia Fever | None | + / + | + | Diffuse capillaritis discrete bilateral papilledema | Intravenous MP pulse 15 mg/kg and oral prednisone Infliximab 5 mg/kg Azathioprine 2 mg/kg/day Colchicine 1 mg/day | Dexamethasone subconjunctival injection Hourly Dexamethasone eyed drops Tropicamide eye drops | + | + | 24 |
3 | 14 / F | Northern Africa HLAB51 + | OD: 0.2 OS: 0 | OD: 0 OS: 0 | Neurological: Encephalomyelitis with aseptic meningitis | 21 | Encephalomyelitis with aseptic meningitis polyarthralgia | - None | -—/ + | + | Macular edema Vasculitis Papillitis | Intravenous MP pulse 15 mg/kg and oral prednisone Infliximab 5 mg/kg Azathioprine 2 mg/kg/day Colchicine 1 mg/day | Dexamethasone eye drops (6/day) | - | - | 57 |
4 | 16 / M | Northern Africa HLAB51- | OD: 2.7 OS: 0.7 | OD: 3 OS: 3 | Ocular | 6 | Oral aphtosis Cerebral venous sinus thrombosis Psychiatric manifestations Anorexia | None | + / + | + | Ischemic retinopathy with necrotizing retinitis Optic neuritis Occlusive vasculitis | Intravenous MP pulse 15 mg/kg and oral prednisone Infliximab 5 mg/kg Cyclophosphamide 750 mg/day Azathioprine 2 mg/kg/day Colchicine 1 mg/day Enoxaparin 150UI/day | Dexamethasone eye drops (4/Day) | + | + | 104 |